遗传性共济失调是一组共济运动障碍为突出表现的中枢神经系统变性疾病 ,常有家庭史 ,分型较复杂 ,现将笔者遇到一型“遗传性痉挛性共济失调”一家系报道如下。1　临床资料先症者 ,女 ,4 2岁 ,因双下肢无力 ,步态不稳 ,双上肢粗震颤 10年 ,加重伴不能行走 ,进食呛咳 1年入院。查 Hereditary ataxia is a group of disorders of the ataxia for the outstanding performance of CNS degenerative diseases, often family history, classification is more complicated, now I encountered a type of “hereditary spastic ataxia” a family Reported as follows. 1 clinical data first symptom, female, 4 2 years old, due to weakness of both lower extremities, unsteady gait, upper extremities rough tremor 10 years, aggravated with can not walk, eat cough 1 year admission. check