目的:探讨Shy-Drager的早期诊断,避免误诊。方法:对14例Shy-Drager综合征患者的临床资料进行回顾性分析。结果:14例患者在早期或首次就诊中均存在误诊,且误诊分别发生在泌尿外科、心内科、神经内科等各科室,误诊病种多样。结论:自主神经功能异常是Shy-Drager综合征的临床特点,测量卧立位血压可有效避免早期误诊的发生。 Objective: To investigate the early diagnosis of Shy-Drager and avoid misdiagnosis. Methods: The clinical data of 14 patients with Shy-Drager syndrome were retrospectively analyzed. Results: All the 14 patients were misdiagnosed in early or first visit, and the misdiagnosis occurred in various departments such as urology, cardiology and neurology, respectively. The misdiagnosis varied. Conclusion: The dysfunction of autonomic nervous system is a clinical feature of Shy-Drager syndrome. Measurement of lying position blood pressure can effectively prevent the early misdiagnosis.