目前本病报告150多个家系,为常染色体显性遗传。Usher等及其同事认为本病主要是通过男性传递给后代。由患病女性传递者少见。Moraine等人描述的家族中患病女性均有原发或继发闭经,或是有月经不规则。Zlotogora等人在对一个家系研究和以前报告的38个家系分析之后指出,本病存在着两种类型。Ⅰ型:即普通型。只通过患病男性传递。Ⅱ型:是患病男女双方均可传递。两型均可男-男传递,两型都以常染色 The current disease reports more than 150 families, autosomal dominant. Usher and colleagues think the disease is passed on to males mainly from offspring. Rare female transmission by the sick. Moraine et al. Describe the presence of primary or secondary amenorrhea in women affected by the family, or irregular menstruation. After analyzing a pedigree study and 38 previously reported pedigrees, Zlotogora et al. Pointed out that there are two types of this disease. Type Ⅰ: that is ordinary type. Passed only by sick men. Ⅱ type: both male and female patients can be passed. Both types can be male - male transmission, both types are often stained