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背景 大网膜原发苗勒氏管混合瘤很少见 ,迄今为止仅报道了 2例 ,具有其特殊临床特征。病例 女性 ,6 7岁 ,G6P5 ,主因腹痛、腹胀 15天就诊于北京大学人民医院妇科。体格检查发现一直径 12厘米腹部包块 ,活动度差。行肿瘤及大网膜大部分切除 ,全子宫加双附件切除术。术后病理示大网膜原发恶性苗勒氏管混合瘤。术后顺铂、吡喃阿霉素、足叶已甙化疗一疗程 ,因严重骨髓抑制 ,未继续化疗 ,术后 8个月发现肿瘤肝转移。结论 原发性恶性苗勒氏管混合瘤预后差 ,现今手术仍是最有效的治疗手段 ,化疗及放疗效果不确切。
Background Omental primary Müllerian mixed tumor is rarely seen, only 2 cases have been reported so far, with its special clinical features. Case of women, 6 7 years old, G6P5, mainly due to abdominal pain, abdominal distension 15 days visit Peking University People’s Hospital gynecology. Physical examination found a diameter of 12 cm abdominal mass, poor activity. Tumors and omentum resection most of the whole hysterectomy plus double attachment resection. Postoperative pathology showed omental primary malignant Mullerian mixed tumor. Postoperative cisplatin, pirarubicin, folium glycosides chemotherapy for a course of treatment, due to severe bone marrow suppression, did not continue chemotherapy, 8 months after the discovery of liver metastases. Conclusions The primary malignant Millelle’s disease has a poor prognosis. Today’s surgery is still the most effective treatment and the effects of chemotherapy and radiotherapy are not clear.