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本文描述5例萎缩性肌强直症妇女的妊娠,其中4例严重影响了婴儿,并复习了有关资料,4例新生儿中有3例于生后3周死于呼吸衰竭。第4例婴儿目前为4个月,有呼吸及吞咽困难。由于妊娠而使症状恶化,常因自然流产,早产及新生儿疾病使胎死率增高。产程延长为常见之合并症。许多患有萎缩性肌强直症之新生儿并无症状,然而严重受侵新生儿之异常与母体疾病程度无关其临床表现为关节弯曲,尤以两下肢明显,周身张力减退及咽肌软弱。较少见之现象为羊水过多,两侧面神经及膈肌麻痹,呼吸衰竭,胃肠蠕动减少,先天
This article describes the pregnancies of 5 women with atrophic myotonia, of which 4 seriously affected infants and reviewed the data, 3 of 4 neonates who died of respiratory failure 3 weeks after birth. The fourth case of infants is currently 4 months, breathing and swallowing difficulties. Due to pregnancy and make the symptoms worse, often due to spontaneous abortion, premature birth and neonatal diseases make fetal mortality increased. Labor prolongation as a common complication. Many newborns with atrophic myotonia are asymptomatic, yet the severely affected newborn has nothing to do with the degree of maternal disease. The clinical manifestations are joint flexion, especially in both lower extremities, with decreased global tension and pharyngeal muscle weakness. Less common phenomenon of polyhydramnios, facial nerve and diaphragm paralysis on both sides, respiratory failure, decreased gastrointestinal motility, innate