肥厚性梗阻型心肌病(HOCM)又称特发性肥厚性主动脉瓣下狭窄(IHSS),是一种较少见的原发性心肌病,往往在一个家族内同时有数名成员得病。我们曾对1例患者的第一级亲属进行调查,发现2人患病,2人可疑。特报道如下。例1:先证者,男性,22岁,工人,一向无明显症状,最近因偶感胸闷查心电图疑为“陈旧性前壁心肌梗塞”。体检:血压110/70毫米汞柱,心率70次/分,律整,心尖区可闻2/6级收缩中期喷射性杂音,向左下胸骨缘传导,有第四心音,心尖可触及双重搏动,无震颤。心电图:左前分支阻滞,左胸前导联有较深Q波,但宽度不超过0.04秒,R波 Hypertrophic obstructive cardiomyopathy (HOCM), also known as idiopathic hypertrophic aortic stenosis (IHSS), is a rare primary cardiomyopathy, often having multiple members in one family at the same time. We conducted a survey on the first-degree relatives of one patient and found that two were affected and two were suspicious. Special report as follows. Example 1: Proof, male, 22 years old, worker, has no obvious symptoms, recent occasional chest tightness check electrocardiogram as “old anterior myocardial infarction.” Physical examination: blood pressure 110/70 mm Hg, heart rate 70 beats / min, the whole law, the apex area can be heard 2/6 contraction mid-term jet murmur, conduction to the left lower chest bone edge, a fourth heart sound, apical palpable double beats, No tremor. ECG: Left anterior branch block, the left chest lead with a deeper Q wave, but the width of no more than 0.04 seconds, R wave