弥漫性肺间质疾病 (interstitiallungdisease,ILD)是以肺泡壁为主并包括肺泡周围组织及其相邻支撑结构发生病变的一组疾病 ,以慢性炎症和间质纤维化为主要病理特征 ,一般按已知病因和未知病因将其分为两大类。特发性肺间质纤维化(idiopathicpulmonaryfibrosis ,IPF)是原因不明 Diffuse interstitial lung disease (interstitiallungdisease, ILD) is mainly in the alveolar wall and includes alveolar tissue and its adjacent support structure lesions of a group of diseases, chronic inflammation and interstitial fibrosis as the main pathological features, usually by Known etiology and unknown causes will be divided into two categories. Idiopathic pulmonary fibrosis (idiopathicpulmonary fibrosis, IPF) is unknown