先天性肝内胆管囊性扩张是青少年漫性胆囊结石和肝内结石的一种罕见原因。本病的治疗较困难。作者采用长期口服熊去氧胆酸（ursodeoxycholicacid）治疗肝内结石取得满意效果。12例Caroll氏综合征伴肝内结石的患者长期使用能去氧胆酸治疗，用量为每天10～20mg从g。12例患者中， Congenital intrahepatic bile duct cystic dilatation is a rare cause of diffuse gallbladder stones and intrahepatic stones in adolescents. The treatment of this disease is more difficult. The authors used long-term oral ursodeoxycholic acid (ursodeoxycholicacid) treatment of intrahepatic stones with satisfactory results. 12 cases of Caroll’s syndrome with intrahepatic stones in patients with long-term use of deoxycholic acid treatment, the amount of 10 ~ 20mg per day from g. Of the 12 patients,