论文部分内容阅读
Stiff-man(僵直人)综合征少见于成人,特点有进行性强直及中轴和肢体肌肉系统痛性痉挛伴有休息时有连续运动性活动的肌电图表现。病因不清,但伴有糖尿病和甲状腺毒症。这种内分泌紊乱的治疗不能缓解神经肌肉症状。作者等报告一例有Sti-ff-Man综合征的临床和电生理特点伴ACTH,GH和催乳素缺乏。用皮质醇替代治疗其强直得到缓解。 42岁女性,1979年妊娠期间出现严重弥漫性头疼,继之痛性下肢痉挛数月。正常分娩后无严重产
Stiff-man syndrome is uncommon in adults and is characterized by progressive ankylosis and painful spasticity of the central and limb musculature with electromyographic performance of continuous motor activity at rest. The cause is unclear, but with diabetes and thyrotoxicosis. This treatment of endocrine disorders does not relieve neuromuscular symptoms. The authors report an example of the clinical and electrophysiological features of Sti-ff-Man syndrome with ACTH, GH and prolactin deficiency. Substitution of cortisol for treatment of tonic relief. 42-year-old woman, a serious, diffuse headache during her pregnancy in 1979, followed by painful lower extremity spasms for months. No serious after normal delivery