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血红蛋白H病(以下简称HbH病),于1955年首先由Rigas等在属同一家族的两个华侨中发现,以后在东南亚、非洲、欧洲等民族中亦有发现。海外华侨屡见报导,广东省亦不少见。我院在1976年夏季组织医疗队到广州市郊某一公社普查贫血29,531人,发现贫血92例,其中轻型β地中海贫血6例,重型β地中海贫血3例,血红蛋白H病6例。血红蛋白H病在该地区的发病率超过0.002%。现将我院血液病小组在1975年3月～1977年8月,共发现HbH病35例的临床表现,实验室检查及就诊误诊作一概要分析,汇报如下:
Hemoglobin H disease (hereinafter referred to as HbH disease) was first discovered by Rigas et al. In two overseas Chinese members of the same family in 1955 and later in Southeast Asia, Africa and Europe. Overseas Chinese are frequently reported that Guangdong is not uncommon. In the summer of 1976, our hospital organized a medical team to survey 29,531 anemic people in a commune in the suburbs of Guangzhou. Anemia was found in 92 cases, including 6 cases of light β-thalassemia, 3 cases of β-thalassemia major and 6 cases of hemoglobin H disease. The prevalence of hemoglobin H disease in the area is over 0.002%. Now our hospital blood disease group in March 1975 ~ August 1977, a total of 35 cases of HbH disease were found in the clinical manifestations, laboratory examinations and misdiagnosis as a summary analysis, reported as follows: