Caroli病为先天性肝内胆管囊状扩张,有时亦有肝外胆管扩张,并可伴肝纤维化或门脉高压。用侵入性内窥镜逆行胆管造影或经皮肝穿刺胆管造影可诊断此病。 Caroli disease is cystic dilatation of the congenital intrahepatic bile duct, and sometimes extrahepatic bile duct dilatation, and may be associated with liver fibrosis or portal hypertension. With invasive endoscopic retrograde cholangiography or percutaneous transhepatic cholangiography can diagnose the disease.