近20年,对肥厚性心肌病(HC)进行了大量研究,猝死是肥厚性心肌病的主要问题之一。年死亡率为3～5％。年轻患者伴晕厥史及有猝死家族史者,其预后不良。肥厚性心肌病患者心跳骤停的原因意见不一。1957年,Brock推测严重左室肥厚的患者心跳骤停是由于心脏射血时,左室流出道梗阻突然增加所致。①猝死虽可发生任何年龄,但年轻患者更易发生。原发性心肌损 In the past 20 years, a great deal of research has been done on hypertrophic cardiomyopathy (HC). Sudden death is one of the main problems of hypertrophic cardiomyopathy. The annual mortality rate is 3 ~ 5%. Young patients with syncope history and family history of sudden death, the poor prognosis. Hypertrophic cardiomyopathy patients with different reasons for cardiac arrest. In 1957, Brock speculated that cardiac arrest in patients with severe left ventricular hypertrophy resulted from a sudden increase in left ventricular outflow tract obstruction as a result of cardiac ejection. Although sudden death may occur at any age, but younger patients are more likely to occur. Primary myocardial damage