非对称性室间隔肥厚又称原发性梗阻型心肌病、特发性肥厚性主动脉瓣下狭窄、肥厚性梗阻型心肌病等。是原发性心肌病的一种较为少见的类型,确切的发病率不太清楚,美国某地区每年以心导管为主的综合性检查2800例以上,发现本病占1％。从患者第一级亲属(first degree relative——父母、兄弟姊妹和子女)的调查表明,本病系常染色体显性基因所控制的心肌遗传缺陷,其特征为室间隔明显地增厚。大量肥厚 Asymmetrical ventricular septal hypertrophy, also known as primary obstructive cardiomyopathy, idiopathic hypertrophic aortic stenosis, hypertrophic obstructive cardiomyopathy and so on. Is a relatively rare type of primary cardiomyopathy, the exact incidence is not clear, the United States every year a catheter-based comprehensive examination of more than 2800 cases and found that the disease accounted for 1%. Surveys of first degree relatives (parents, siblings, and children) indicate that this disease is a cardiomyopathic defect controlled by an autosomal dominant gene that is characterized by a marked increase in ventricular septum. A lot of hypertrophy