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肺动脉高压(Pulmonary Arterial Hypertension,PAH)是以小肺动脉的血管增生和重构为主要特征的一种疾病[1]。它导致肺血管阻力进行性增加,是引起右心衰和成年前死亡的原因之一。肺动脉高压是指安静时肺动脉压25mmHg[lmmHg=0.1333KPa]或运动时30mmHg。肺动脉高压包括原发性肺
Pulmonary Arterial Hypertension (PAH) is a disease characterized mainly by the proliferation and remodeling of small pulmonary arteries [1]. It causes a progressive increase in pulmonary vascular resistance and is one of the causes of right heart failure and premature mortality. Pulmonary hypertension refers to pulmonary arterial pressure when resting 25mmHg [lmmHg = 0.1333KPa] or exercise 30mmHg. Pulmonary hypertension includes primary lungs