马凡氏综合征(Marfan’s syndrome)是一种先天性遗传性疾病,临床表现多种多样,发病率为2～10/10万。此病常伴有严重的心血管疾病,现将3例报告如下。例1,曹某,男,28岁,因胸痛、气短3个月急诊入院。患者于入院前3个月在劳动中突然感到胸前区撕裂样剧痛,6小时后缓解。血压126/34mmHg,消瘦,身高175cm,指间距179cm,坐高80cm,蜘蛛足样指(趾)。鸡胸,心尖搏动(氵弥)散,胸骨左缘第3、 Marfan’s syndrome is a congenital hereditary disease with a variety of clinical manifestations, with an incidence of 2 to 10 per 100,000. The disease is often accompanied by severe cardiovascular disease, the report of 3 cases are as follows. Example 1, Jo, male, 28 years old, due to chest pain, shortness of breath 3 months emergency admission. Patients in the labor 3 months before admission suddenly felt a sharp tear in the chest area, 6 hours after the relief. Blood pressure 126 / 34mmHg, weight loss, height 175cm, finger spacing 179cm, sitting height 80cm, spider foot-like means (toe). Chicken breast, apex beat (Mi Mi) scattered, the left sternal third,