有一项小鼠的研究提示,在肺中一种称为神经酰胺的脂肪化合物的蓄积会引起慢性肺囊性纤维化感染.该发现对于这种遗传性疾病尚未解决的病程来说又增加了一个曲折.患有囊性纤维化的病人含有CFTR基因突变.这个基因所编码的蛋白质,正常时使离子如穿梭般地往返于细胞内外,而引领这种? A mouse study suggests that the accumulation of a fatty compound called ceramide in the lung can cause chronic pulmonary cystic fibrosis, an increase of an unresolved course of the hereditary disease Twists and turns Patients with cystic fibrosis contain a mutation in the CFTR gene, a protein encoded by this gene that normally leads ions to and fro within the cell, shuttling back and forth, leading the way.