延髓脊髓空洞症是比较常见的疾病,但家族性发病者少见,作者见到6例,报告如下。 病例摘要 例1 女、18岁、于8年前无诱因出现左上肢麻木,并逐年加重。5年前发现左背部及左手背部起水泡,无疼痛及痒感。左上臂皮肤有2cm~2烫伤后愈合疤痕。胸椎轻度左凸。左面部痛温觉减退,左C_1～L_5痛温觉减退,触觉存在。四肢肌张力,肌力、肌 Medulla oblongata is a more common disease, but rare in familial onset, the authors see 6 cases, the report is as follows. Case summary 1 female, 18 years old, no incentive to appear eight years ago left upper limb numbness, and increased year by year. 5 years ago found the left back and left back blisters, no pain and itching. Left upper arm skin 2cm ~ 2 scars heal after scalding. Thoracic mild left convex. Left facial pain hypothermia, left C_1 ~ L_5 pain decreased, tactile presence. Limb muscle tension, muscle strength, muscle