先天性肝纤维化是一种少见的先天性肝脏疾病。国内尚未见报道,本院1977年11月收治一例,生前未获诊断,死后剖检证实。报道如下: 临床资料 男性,24岁,纱厂工人。因中上腹饱胀伴纳差、恶心、腹水进行性增多七个月,黑便一次,血压下降而于1977年11月30日急诊入院。往健,起病于1977年4月,中上腹饱胀、恶心、返酸伴食欲减退,每 Congenital liver fibrosis is a rare congenital liver disease. Not yet reported in China, our hospital in November 1977 admitted to a case, was diagnosed before his death, post-mortem autopsy confirmed. Reported as follows: Clinical data Male, 24 years old, mill workers. Because of abdominal fullness with anorexia, nausea, ascites progressive increase of seven months, black then, blood pressure dropped in November 30, 1977 emergency admission. To health, the onset in April 1977, in the abdomen fullness, nausea, backache with loss of appetite, each