本病罕见,国内曾报告两例,本院收治一例报告如下。患者男,8岁。四个月前开始间歇性全程血尿,伴尿频、尿急、尿痛及排尿困难,20天来症状加重,尿淋漓不尽,阵发性哭闹不安,下腹发现鹅蛋大包块,逐渐增大。无排石史。体检:体温37.2℃,脉搏92次/分,血压120/90mmHg,发育正常,营养尚可,眼睑轻微浮肿,心肺正常。肝脾未触及。双肾未触及,无叩击 The disease is rare, China has reported two cases, the hospital admitted a case report as follows. Patient male, 8 years old. Four months ago began intermittent hematuria, with frequent urination, urgency, dysuria and dysuria, 20 days to aggravate the symptoms, dripping urine, paroxysmal crying uneasy, found the goose large egg mass, gradually increased Big. No row of stone history. Physical examination: body temperature 37.2 ℃, pulse 92 beats / min, blood pressure 120 / 90mmHg, normal development, nutrition is acceptable, slightly eyelid edema, normal heart and lung. Liver and spleen not touched. Kidney not touched, no percussion