小儿阿狄森氏病为罕见疾病,国内报告不多,我科自60年代以来收治20多例,现将资料较完整的15例报告如下。诊断标准:(1)典型临床表现,经肾上腺皮质激素治疗有效。(2)24小时尿17羟皮质类固醇,17酮皮质类固醇降低。(3)血浆皮质醇降低。一般资料:男8例,女7例,男女之比为1.4:1。 Pediatric Addison’s disease is a rare disease, the domestic report is not much, our department since the 60’s admitted more than 20 cases, the data is now more complete 15 cases are reported as follows. Diagnostic criteria: (1) typical clinical manifestations, the effective treatment of adrenal cortex hormones. (2) 24-hour urinary 17 hydroxy corticosteroids, 17 keto-steroids reduced. (3) decreased plasma cortisol. General information: 8 males and 7 females, the ratio of men to women is 1.4: 1.