花生四烯酸(AA)代谢是血小板内一条重要的生化反应途径,其多种代谢产物参与血小板的活化和血管收缩。血小板内有多种酶参与 AA 代谢,近年研究发现有些出血性疾患是由于这些酶缺陷所致,迄今为止在我国尚未见有关报告,现将我院近来发现的一例血栓索(Tx)合成酶缺陷患者报告如下。 Arachidonic acid (AA) metabolism is an important biochemical reaction pathway in platelets, many of its metabolites involved in platelet activation and vasoconstriction. Platelets have a variety of enzymes involved in AA metabolism, recent studies found that some bleeding disorders are due to these enzyme defects, so far in our country have not seen the report, now our hospital recently found a case of thrombus (Tx) synthase defects Patients report as follows.