论文部分内容阅读
鲁登巴赫综合征(Lutembacher syndrome,简称LS)是一种罕见的先天性心脏畸形。我院1975年到1989年12月行心内直视手术800例,其中房间隔缺损(ASD)修补术110例,共发现鲁登巴赫综合征4例,术前均经超声准确诊断。 资料与方法:本组4例,男1例,女3例,年龄12～39岁。临床表现主要有运动性心慌气短、颈静脉怒张、胸廓畸形、口唇轻度紫绀、心界向右扩大、心尖区舒张期杂音、收缩期杂音、胸骨左缘第2肋间闻及收缩期杂音。采用仪器为SSD-800扇扫仪和Mark600双功能显像仪,探头频率3.0MHz,常规切面观察心内结构。 超声表现:(1)4例均示右室扩大,并左、右房扩大2例。(2)房间隔中部均有回声中断。缺损大小为3.2～4.7cm。(3)二尖瓣均示增厚,其中前后瓣同向
Lutembacher syndrome (LS) is a rare congenital heart disease. Our hospital from 1975 to December 1989 underwent open heart surgery in 800 cases, of which 110 cases of atrial septal defect (ASD) repair, were found in 4 cases of Rüdensbach syndrome, preoperative ultrasound were accurately diagnosed. Materials and Methods: The group of 4 patients, 1 males and 3 females, aged 12 to 39 years. The main clinical manifestations of sports palpitation shortness of breath, jugular vein engorgement, thoracic deformity, lips mild cyanosis, the heart to the right to expand, apex diastolic murmur, systolic murmur, sternal left intercostal space smell and systolic murmur . Using the instrument for the SSD-800 fan scanners and Mark600 dual-function imaging device, the probe frequency 3.0MHz, conventional section observation of the heart structure. Ultrasound findings: (1) 4 cases showed right ventricular enlargement, and left and right atrial enlargement in 2 cases. (2) Echogenic interrupt in central atrial septum. Defect size of 3.2 ~ 4.7cm. (3) Mitral valve showed thickening, with the same before and after the valve