上皮样血管内皮细胞瘤是一种少见的血管源性肿瘤,好发于肝脏、肺、骨、头颈部以及软组织等部位。目前国内外文献尚未见发生于臂丛神经束膜血管内的病例报道。本文报告1例发生于臂丛神经束膜结缔组织血管内的上皮样血管内皮细胞瘤,并结合文献对其临床症状、影像学表现、组织病理特征和治疗方案以及预后进行讨论。 Epithelioid hemangioendothelioma is a rare tumor of vasogenic origin that occurs in the liver, lung, bone, head and neck, and soft tissue. At present, no literature has been reported in the cases of brachial plexus vascular. This article reports one case of epithelioid hemangioendothelioma that occurs in the brachial plexus connective tissue vessels and discusses the clinical symptoms, radiographic features, histopathological features, treatment options, and prognosis in combination with the literature.