目的　分析 5 0例经手术后病理证实为颅底部脊索瘤的CT及MR表现 ,提高对该病的认识。方法　男性 34例 ,女性 2 6例 ,全部行MR平扫及增强扫描 ,部分病例同时做了CT扫描及DSA检查。结果　其影像学表现如下 :①发生部位主要位于斜坡 ,鞍旁 ,并可见周围结构联合受累者 ;②肿瘤的形态为不规则形、分叶状 70 % ;③MR影像上主要为长T1,长T2 信号 ,内部结构以不均匀为主 ;④CT上主要为不均匀稍高密度影 ,肿瘤内可见不规则形钙化影 ;⑤病灶周围可见伴有不同程度的骨质破坏 6 8% ;⑥于MR增强扫描时 80 %病例明显强化。结论　MR影像对诊断颅底脊索瘤显示清楚 ,诊断确切 ,但CT显示骨破坏及钙化情况较MR清楚 ,二者可互补。 Objective To analyze the CT and MR findings of 50 cases of postoperative pathologically confirmed chordoma at the base of the skull and to improve their understanding of the disease. Methods There were 34 males and 26 females, all underwent MR plain scan and enhanced scan. CT scan and DSA were performed in some cases at the same time. The results of its imaging findings are as follows: ① The site of occurrence is mainly located in the slope, the parasellar, and visible involvement of peripheral structures; ② The shape of the tumor is irregular, lobulated 70%; ③ MR images mainly long T1, long T2 Signal, the internal structure of the main non-uniform; ④CT uneven mainly for high density, uneven visible calcification in the tumor; ⑤ lesions around the visible with varying degrees of bone destruction 68%; ⑥ enhanced MR 80% of cases were significantly enhanced during the scan. Conclusion MR imaging of the diagnosis of skull base chordoma showed clear, the diagnosis is accurate, but CT showed bone destruction and calcification than MR clear, both complementary.