本文对30例（国内文献28例及本院2例）卵巢环状小管性索瘤进行分析。年龄6～59岁，平均22岁，主要临床表现为性激素紊乱（月经不规、经后出血及性早熟）和腹部肿块，仅1例伴有胃肠道息肉病和皮肤粘膜色素斑。组织学特征为单层和复层小管，管周有基底膜样物环绕，瘤细胞呈条索状或巢状并见核分裂相，可能是形态学恶性特征。 In this paper, 30 cases (28 cases of domestic literature and 2 cases of this hospital) of ovarian ring-shaped tubular glioma were analyzed. Aged 6 to 59 years old, average 22 years old, the main clinical manifestations of sex hormone disorders (irregular menstruation, post-menstrual bleeding and precocious puberty) and abdominal mass, only 1 case with gastrointestinal polyposis and mucocutaneous pigment spots. Histological features of monolayer and stratified tubules, tubular basement membrane samples around the week, the tumor cells were cords or nests and see the mitotic phase, may be characterized by malignant morphology.