先天性细小结肠症是新生儿极为罕见的先天性肠道畸形，我院遇到一例，报告如下患儿男．2天，腹胀，呕吐，无大便。第一胎足月顺娩，查体：腹部明显膨隆．可见肠形及肠蠕动波。腹软，可及肠袢．肝脾未及。叩鼓音，移动性浊音阴性。肛门及外生殖器正常，曾给予开塞露一支，胆管出 Congenital small bowel disease is extremely rare neonatal congenital intestinal malformations, a case of our hospital, the following report male patients. 2 days, bloating, vomiting, no stool. The first full-term delivery of childbirth, physical examination: abdominal bulging. Visible intestinal and peristaltic wave. Abdomen soft, and intestinal gizzard. Liver and spleen not yet. Drum sound, mobility dullness negative. Anus and genitals normal, had given Kaiser exposed, bile duct out