特发性肺含铁血黄素沉着症(IdiopathiePulmonary Hemosiderosis,以下简称IPH),是一种少见的反复发作的肺泡出血,引起含铁血黄素在肺内异常沉积的疾病。本病多见于小儿,病因尚不清楚,早期不易确诊。近几年来国内外陆续报道。我科自1977年3月～1986年5月共收治14例,均根据临床,胸片,痰或胃液找到含铁血黄素巨噬细胞确诊。现报告如下。 Idiopathie Pulmonary Hemosiderosis (IPH) is a rare recurrent alveolar hemorrhage that causes abnormal deposition of hemosiderin in the lung. The disease more common in children, the cause is not clear, early diagnosis is not easy. In recent years, one after another reported at home and abroad. Our department from March 1977 to May 1986 a total of 14 cases were treated, are based on clinical, chest X-ray, sputum or gastric juice to find hemosiderin macrophages confirmed. The report is as follows.