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目的探讨肺组织病理学检查在儿童间质性肺疾病诊断中的意义。方法对2000—2007年北京儿童医院收治的26例不明原因儿童间质性肺疾病肺活检病例进行病理分析。结果26例患儿病理诊断结果:非特异性间质性肺炎6例,闭塞性细支气管炎伴机化性肺炎6例,普通型间质性肺炎、郎格罕组织细胞增生症、淋巴瘤、卡氏肺囊虫肺炎各2例,淋巴细胞性间质性肺炎、肺泡蛋白沉积症、类脂性肺炎、弥漫性泛细支气管炎、呼吸性细支气管炎间质性肺病、闭塞性细支气管炎各1例。结论进行肺组织病理学检查对确诊间质性肺疾病的病因及指导临床治疗有重要意义。
Objective To investigate the significance of lung histopathology in the diagnosis of children with interstitial lung disease. Methods A total of 26 cases of lung biopsy in children with unexplained childhood lung biopsy in Beijing Children’s Hospital from 2000 to 2007 were analyzed. Results 26 cases of pathological diagnosis of children: non-specific interstitial pneumonia in 6 cases, bronchiolitis obliterans with organic pneumonia in 6 cases, common interstitial pneumonia, Langerhan histiocytosis, lymphoma, card Pneumocystis pneumonia in 2 cases, lymphocytic interstitial pneumonia, pulmonary alveolar proteinosis, lipoid pneumonia, diffuse panbronchiolitis, respiratory bronchiolitis interstitial lung disease, bronchiolitis obliterans each 1 example. Conclusion Pulmonary histopathology is important for the diagnosis of interstitial lung disease and clinical treatment.