儿童特发性肺含铁黄素沉着症(IPH)是一组肺泡毛细血管出血性疾病,常反复发作,并以大量含铁血黄素积累于肺内为特征。对该病缺乏认识或认识不足,将延误该病诊断,影响患儿肺纤维化过程及预后。本文从临床特征、诊断等方面分析该病,目的在于加深对该病的认识,提高患儿生存率。1病 Idiopathic pulmonary luteinosis (IPH) is a group of alveolar capillary hemorrhagic disease that is frequently recurrent and characterized by massive accumulation of hemosiderin in the lungs. Lack of understanding of the disease or lack of knowledge, will delay the diagnosis of the disease, affecting children with pulmonary fibrosis and prognosis. This article analyzes the clinical features, diagnosis and other aspects of the disease, the purpose is to deepen the understanding of the disease and improve the survival rate of children. 1 disease