无脉症,又称主动脉弓综合症,以女性多见。病变主要分布在主动脉弓及其分枝,特别是颈动脉起始处和锁骨下动脉,但主动脉的任何部位均可受累。在个别病例,可见有肺动脉、肾动脉、冠状动脉甚至心脏瓣膜受累的证据。最初为动脉周围炎,继而发展为全动脉炎。镜下可见圆细胞浸润,弹力层破坏。最后纤维组织增生,导致血管狭窄,晚期可有钙化。有人认为本病病因是机体对结核菌素的过敏表现或者是风湿病的一部 A pulse-free syndrome, also known as aortic arch syndrome, more common in women. Lesions mainly in the aortic arch and its branches, especially the beginning of the carotid artery and subclavian artery, but any part of the aorta can be involved. In a few cases, there is evidence of involvement of the pulmonary artery, renal artery, coronary artery, and even heart valve. Initially for the periarteritis, and then developed into arteritis. Microscopic round cell infiltration, elastic layer damage. The last fiber tissue hyperplasia, leading to vascular stenosis, calcification may have advanced. Some people think that the cause of the disease is the body’s allergy to tuberculin or rheumatoid rheumatoid