肝内胆管粘液腺癌临床罕见,现报告1例肝内胆管粘液腺癌致反复急性胆管炎发作诊断困难。报告如下。女性,57岁。患者因发作性上腹绞痛20年,伴黄疸、发热3d,于1995年9月以“梗阻性黄疸”收入院。术前B超、CT等检查示肝内外胆管扩张,ERCP造影胰管正常,胆总管直径2.3cm,其上段有多发 Intrahepatic bile duct mucinous adenocarcinoma is rare clinically, and it is reported that one case of intrahepatic bile duct mucinous adenocarcinoma caused by repeated acute cholangitis is difficult to diagnose. The report is as follows. Female, 57 years old. The patient was admitted to the hospital with “obstructive jaundice” in September 1995 due to paroxysmal epigastric colic for 20 years with jaundice and fever. Preoperative B-ultrasonography, CT, etc. showed intrahepatic bile duct dilatation, ERCP pancreatic duct was normal, diameter of common bile duct was 2.3cm, and upper segment had multiple lesions.