1　病例服告　患儿 ,男 ,出生 4天。出生后即发现双小腿及双足皮肤缺损 ,即刻送当地医院就诊 ,创面给予油纱包扎 ,4天后急诊收住我科。体查 :患儿神态清 ,精神食欲均差 ,双小腿、膝关节以下至双足趾处无皮肤覆盖 ,表面呈鲜红色肉芽状 ,总面积 8.5 %。诊断为先天性双下肢皮肤缺 1 case of children, male, born 4 days. After birth that double-legged and bipedal skin defect, immediately sent to the local hospital for treatment, the wound to give gauze bandage, emergency room after 4 days admitted to our department. Physical examination: children demeanor, mental appetite were poor, double leg, knee to the next toe no skin cover, the surface was bright red granulation, the total area of ​​8.5%. Diagnosis of congenital absence of both lower extremity skin