本病自1907年Schwabach首先报告以来,从组织学上证实面神经管内或其周围存在横纹肌纤维。晚近的1322具颞骨检查,发现35具存在异位肌纤维,发生率约2.5％。目前尚未发现面神经管内的异位横纹肌对听力、前庭有何影响。Cerny报告3例,手术中发现Bell氏麻痹合并异位肌肉,围绕于面神经第二膝部。其中1例曾考虑为肿瘤。Murata等报告1例下鼓室异位横纹肌合并面瘫,此例的X线、物理检查很像颈静脉球体瘤。本文介绍2例。 Since the first report of Schwabach in 1907, the disease has been histologically confirmed to have striated muscle fibers in and around the facial nerve canal. Nearly 1322 with temporal bone examination found that there are 35 ectopic muscle fibers, the incidence of about 2.5%. No effect of ectopic striated muscle in facial nerve tube on hearing and vestibule has been found. Cerny report 3 cases, surgery found Bell’s paralysis with ectopic muscles, around the second facial facial nerve. One case was considered as a tumor. Murata et al reported a case of ectopic rhabdomyostenosis with facial paralysis, this case of X-ray, physical examination is very similar to the jugular bulb tumor. This article describes two cases.