目的　初步明确肺外小细胞癌（ＥＰＳＣＣＡ）的诊断与治疗原则。方法　对经病理确诊的１４例肺外小细胞癌作回顾性分析。结果　有明确分期的ＥＰＳＣＣＡ １０例，其中局限期３例，１年生存率６６．７％（２／３）；广泛期７例，中位生存期９个月，１年生存率４２．９％（３／７）。结论　ＥＰＳＣＣＡ易早期播散转移，治疗前应行系统检查，综合治疗是主要治疗手段。 Objective To identify the principles of diagnosis and treatment of extra-small cell lung cancer (EPSCCA). Methods A retrospective analysis of 14 extrapulmonary small cell carcinomas confirmed by pathology was performed. Results There were 10 patients with clearly staged EPSCCA, of which there were 3 patients with a limited period of 1 year survival rate of 66.7% (2/3); 7 patients with extensive period, a median survival period of 9 months, and 1 year survival rate of 42.9% (3/7). Conclusions EPSCCA is easy to spread and metastasize early. Systematic examination should be performed before treatment. Comprehensive treatment is the main treatment.