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本病症首先被Aufcy(1893年)所注意,Ha-llermann(1948年),Streiff(1954年)和Fran-cois(1958年,1960年)对本病作过较详细的描述,故后人分别以他们的名字命名。病人以发育不全的下颌和突出的鹦鹉状鼻子给人以“鸟面”的印象。临床有头颅颜面骨发育不全,先天性白内障,小眼球,小角膜、眼球震颤、斜视等表现。病因未明,遣传方式也未定,多为散发性.现将我们最近遇到的一例报告如下. 病者张××,男, 33岁,因下颌短小,牙列拥挤由眼科转诊至口腔科。患者自幼视朦,双眼瞳孔区呈白色,并行斜视和眼球震颤。10年前因“晶体
The condition was first noted by Aufcy (1893), which was described in more detail by Ha-llermann (1948), Streiff (1954) and Fran-cois (1958, 1960) Named after them. The patient gave the impression of “bird's face” with an under-developed jaw and a prominent parrot-like nose. Clinical skull facial hypoplasia, congenital cataracts, small eyeball, small cornea, nystagmus, strabismus and other performance. The etiology is unknown, the mode of dispatching also undetermined, mostly sporadic.Now we recently encountered a case report as follows: The patient Zhang × ×, male, 33 years old, due to short mandibular dentition crowded by ophthalmology referral to stomatology . As early as the patient Meng, his pupil area was white, parallel strabismus and nystagmus. 10 years ago because of "crystal