进行性半侧颜面萎缩症,是一种较少见的面部畸形。本病主要侵犯皮肤、皮下组织、脂肪、肌肉和骨骼,形成颜面部严重的进行性萎缩畸形,且伴有局部色素沉着和感觉异常,以至口、眼、鼻等器官的功能障碍。由于病因不明,治疗困难,至今仍无特效疗法。近几年来,由于显微外科技术的发展,有人主张在病变静止后试用组织游离移植充填治疗,我们应用直视下小血管吻合大网膜游离移植术,矫正半侧颜面萎缩畸形,改善部分临床症状,初步取得成功,现报道如下。 Progressive hemifacial atrophy, is a less common facial deformity. The main invasion of the disease skin, subcutaneous tissue, fat, muscle and bone, the formation of facial severe progressive deformity deformity, and accompanied by local pigmentation and sensory abnormalities, as well as mouth, eyes, nose and other organ dysfunction. Due to unknown etiology and treatment difficulties, there is no effective therapy. In recent years, due to the development of microsurgical techniques, some people advocate the trial of free tissue graft transplantation after the rest of the lesion, we apply direct vision under the small vessel anastomosis omentum surgery, correction of facial hemivertebra deformity, to improve some of the clinical Symptoms, the initial success, are reported below.