产后溶血性尿毒症作为一种新的综合征于1968年首先被提出。因病因不明,预后严重,过去国内外对此病缺乏认识,报道很少。1979年Allen 等人统计了世界各地发生的40例报道,其中80%死亡,15%需长期进行透析或肾移值,仅有5%存活。1980年白求恩医大报道3例死亡病例,我院收治的4例也皆死亡。产后溶血性尿毒症已成为威胁产妇生命的疾病之一。现结合文献复习,初步探讨其临床表现、诊断和治疗,以期达到早期诊断、合理治疗、降低死亡率的目的。病例报告 Postpartum hemolytic uremia as a new syndrome was first proposed in 1968. Due to unknown etiology, the prognosis is serious, the lack of awareness of the disease at home and abroad in the past, few reports. In 1979, Allen et al. Reported 40 cases reported worldwide, of which 80% were fatal, 15% needed long-term dialysis or kidney transplant, and only 5% survived. In 1980, Bethune Medical University reported 3 deaths and 4 deaths in our hospital. Postpartum hemolytic uremia has become one of the maternal life-threatening diseases. Now combined with the literature review, preliminary study of its clinical manifestations, diagnosis and treatment, in order to achieve early diagnosis and reasonable treatment, reduce mortality. Case Reports