本文总结62例围产儿先天性畸形尸检资料,包括32例死胎、13例死产和17例死亡新生儿。前三位依次为神经系(41.93％)、颌面部(17.74％)和心血管(9.68％)畸形。多发性者达70.97％,单发性者仅29.03％。多系统畸形占53.22％。有体表畸形者为77.42％,发现内脏畸形者约50％。体表和内脏畸形常同时并存,也可单独发生。6例心血管畸形均为低体重儿。识别畸形,巨检是最简单实用的检查方法。 This article summarizes 62 cases of perinatal congenital anomalies autopsy data, including 32 stillbirths, 13 stillbirths and 17 neonatal deaths. The first three followed by neurological (41.93%), maxillofacial (17.74%) and cardiovascular (9.68%) deformity. 70.97% of those with multiple, only 29.03% of those with solitary. Multiple system malformations accounted for 53.22%. Body surface deformity who was 77.42%, found that about 50% of visceral deformities. Surface and visceral abnormalities often co-exist, but also can occur alone. Six cases of cardiovascular malformations were low birth weight children. Identify deformities, giant check is the most simple and practical method of inspection.