Ehlers-Danlos 综合征(EDS)包含一组不同遗传方式的结缔组织病。特征为皮肤弹性过高、脆性增加、破损后不易愈合,关节过度伸张和内脏变异。本文报告两例同胞兄弟表现为眼-脊柱侧弯型 EDS(即 EDSⅥ型),并伴有多发性周围神经病,作者认为,已构成一种独立的临床实体。例1,先证者,男,23岁。足月顺产,新生儿期全身松软,脊柱侧弯,漏斗胸和皮肤 Ehlers-Danlos syndrome (EDS) contains a heterogeneous group of connective tissue diseases. Characterized by the skin is too high elasticity, increased brittleness, easy to heal after damage, excessive joint extension and visceral variation. This article reports the performance of two siblings as an ocular-scoliotic EDS (EDS VI type) with multiple peripheral neuropathy, which the authors believe has formed an independent clinical entity. Example 1, proband, male, 23 years old. Full-term follow-up, the newborn period loose body, scoliosis, funnel chest and skin