Ｌｅｂｅｒ病是一种遗传性疾病 ,为青少年期急起的双眼视神经病变。我们在临床工作中发现本病一家系 2例。温习文献结合病例综合报道如下先证者 ,王某 ,男 ,1 9岁。因双眼同时视力下降、似雾中视物半月于 1 998-1 2 -2 4入院。体检 :一般情况好 ,心、肺、腹及四肢未见异常。眼 Leber’s disease is a hereditary disease that is an etiological binocular optic neuropathy in adolescence. We found in the clinical work of a family of 2 cases. Comprehensive review of the literature combined with the case reported the following proband, Wang, male, 19 years old. Due to decreased visual acuity both eyes, like fog half moon in the hospital admission of 1 998-1 2 -24. Physical examination: the general situation is good, heart, lung, abdomen and limbs without exception. eye