Moyamoya病又称烟雾病或脑底异常血管网症。在脑血管造影上显示多数异常血管网团,其影像很象吸烟时吐出的烟雾,因此得名。本病的主要病理改变为双侧颈内动脉分叉部原因不明的狭窄或闭塞;成人则以颅内出血为主,如脑室出血,蛛网膜下腔出血等。 1963年铃木二郎在日本22次脑神经外科学会以“Willis氏动脉环闭塞症”为题报告了6个病例,提出异常血管网是由于后天缓慢的脑血管狭窄或闭塞后,侧枝循环形成而引起的血管增生。1969年铃木氏正式以Moy-amoyra病的病名发表文章,并得到了各国学者的公认。自发现本病20年来,国内外都 Moyamoya disease, also known as moyamoya disease or abnormal brain network disease. In cerebral angiography showed most abnormal vascular network group, its image is much like the smoke emitted when smoking, so named. The main pathological changes of this disease are unidentified stenosis or occlusion of the bifacial bifurcation of the internal carotid artery. In adults, intracranial hemorrhage is the main cause, such as ventricular hemorrhage and subarachnoid hemorrhage. In 1963, Jiroiro Suzuki reported six cases in 22 Japanese Society of Neurosurgery Societies on “Willis’s arterial ring occlusion.” He suggested that the abnormal vascular network was caused by the formation of collateral circulation after a slow cerebral vascular stenosis or occlusion Vascular hyperplasia. In 1969, Suzuki officially published an article under the name of Moy-amoyra disease and was recognized by scholars in various countries. Since the discovery of the disease 20 years, both at home and abroad