肝豆状核变性又称Wilson病，临床上颇为少见，我科曾误诊2例，结合有关资料报告分析如下。1病例介绍例1男性，9岁。因反复黄疸，恶心、呕吐、纳差及肝功能异常于1996年6月12日入院。患儿于3年前无诱因出现浓茶色尿、肝肿大、肝功转氨酶200单位，在当地按“肝病”治疗，2月后自 Wilson disease, also known as Wilson’s disease, clinically rare, my department had misdiagnosed in 2 cases, combined with the relevant information reported as follows. A case introduction example 1 male, 9 years old. Due to recurrent jaundice, nausea, vomiting, anorexia and liver dysfunction in June 12, 1996 admission. Children 3 years ago, there was no incentive causes dark brown urine, hepatomegaly, liver transaminase 200 units, according to the local “liver disease” treatment, since February