目的 :了解住院儿童门脉高压症的病因和预后。方法 :回顾性分析 1992年 6月至 2 0 0 0年 6月 8年间收治的儿童门脉高压症 9例 ,病因明确 7例 ,随访 6例 ,随访时间为 0 .5～ 6年。结果 :本组 7例儿童门脉高压症 ,门脉海绵样变 4例 ,肝硬化 2例 ,先天性肝纤维化 1例。门脉海绵样变预后较肝硬化为好。结论 :儿童门脉高压症的病因与成人不同 ,以门脉海绵样变为主 ,其预后与病因有关 Objective: To understand the etiology and prognosis of hospitalized children with portal hypertension. Methods: A retrospective analysis of 9 cases of children with portal hypertension admitted in June, 1992 to June, 2004 with clear etiology in 7 cases and 6 cases were followed up for 0.5-6 years. Results: The group of 7 children with portal hypertension, portal vein sponge-like change in 4 cases, 2 cases of cirrhosis, congenital liver fibrosis in 1 case. Portillo-sponge-like prognosis is better than cirrhosis. Conclusions: The etiology of children with portal hypertension is different from that of adults, with portal-like sponge-like change, and its prognosis is related to the cause