家族性外胚层发育不良是一种少见的遗传性疾病.我院曾遇到2例同胞兄弟,现报告于下. 例1:吴××,男,19岁,杭州人,学生,(见图左1).诉自幼不出汗,无皮脂腺分泌而就诊.平时体温在37.4～37.8℃之间,每到天气炎热时,喜在荫凉通风场所或浸泡在河水中,否则体温上升甚至中暑.平时饮水 Familial ectodermal dysplasia is a rare genetic disease in our hospital has encountered two siblings, the report is now under. Example 1: Wu XX, male, 19 years old, Hangzhou, students, (see Figure Left 1) v. Since childhood, no sweating, no sebaceous gland secretion and treatment. Usually body temperature between 37.4 ~ 37.8 ℃, whenever the weather is hot, like in the shady ventilation or soaking in the river, or body temperature rise or even heat stroke. Usually drink water