例1男,2岁。父母主诉患儿对声音刺激无明显反应,不会说话,于2009年1月来我院就诊。否认耳聋家族史、耳毒性药物及噪声接触史。其母孕龄29岁,体健;患儿足月顺产,出生时无窒息史。体检:生长发育良好。耳科专科检查:双鼓膜正常。听功能测试:双耳鼓室导抗图为“A”型,双耳同侧及交 Example 1 male, 2 years old. The parents complained of children no obvious reaction to the sound stimulation, can not speak, in January 2009 to our hospital. Denied family history of deafness, ototoxic drugs and history of exposure to noise. The mother’s gestational age 29 years old, healthy; full-term children with birth, no history of asphyxia at birth. Physical examination: good growth and development. Ear specialist examination: double tympanic membrane normal. Listen to functional tests: Binaural tympanogram shown as “A” type, both ears ipsilateral and pay