血友病是一类性联隐性遗传性疾病。其中血友病 A(因子Ⅶ缺乏)发病率占出生男性的1/10000;血友病 B(因子Ⅸ缺乏)占血友病发病率的1/4。临床表现两型相似,均为自发性或轻微损伤后出血,包括皮下瘀斑、深部肌肉血肿、关节出血或手术后出血不止,严重者多死于幼童期,部分则留下后遗症。近年来血友 Hemophilia is a type of heritable recessive genetic disease. Incidence of hemophilia A (factor VII deficiency) accounts for 1/10000 of the male birth; hemophilia B (factor IX deficiency) accounts for one-fourth of the incidence of hemophilia. Clinical manifestations of two types are similar, are spontaneous or minor bleeding after injury, including subcutaneous ecchymosis, deep muscular hematoma, joint bleeding or bleeding after surgery more than those who died in severe cases of childhood, while leaving some sequelae. In recent years, hemophilia