Axenfeld-Rieger 综合征是双侧性疾病,其特征为突出的、前移的 Schwalbe 氏线(后胚胎环)和虹膜异常,有半数以上的病人伴有继发性青光眼且疗效不佳。本文报告10例从1982～1986年在本院就诊的该征病例,女性5例,男性5例,年龄在7～40岁,多因继发性青光眼就诊,半数以上有全身异常,主要为牙齿和面部畸形,但10例病人中无一例有家族史,与文献报告不同,可能以散发病例居多。 Axenfeld-Rieger syndrome is a bilateral disease characterized by prominent, advancing Schwalbe’s line (posterior embryonic ring) and iris abnormalities, with more than half of patients with secondary glaucoma and poor outcome. This article reports 10 cases from 1982 to 1986 in our hospital for treatment of this syndrome, 5 cases of women, 5 males, aged 7 to 40 years old, mostly due to secondary glaucoma treatment, more than half of the general anomalies, mainly for the teeth And facial deformities, but none of the 10 patients had a family history, which was different from the literature reports and was likely to be predominantly sporadic.