WG病因不明，多认为与自身免疫有关，特征为伴血管炎的坏死性肉穿肿性炎症，发育率低，男性稍多，30一60岁高发（8一99岁）。儿童病例罕见，迄今文献上尚不足30例记载，其LPIS例累及上呼吸道（喇仅有呼吸道受累）．病变损害部位典型者为具、肺、肾三征（成人．病例中占85呢）， WG etiology is unknown, and more that associated with autoimmune, characterized by necrotizing meat inflammation associated with vasculitis, low rate of development, a little more men, 30-60 years old (8 to 99 years old). Children are rare, so far less than 30 documented in the literature, the LPIS cases involving the upper respiratory tract (la only airway involvement). Lesions lesions typical of those with, lung, kidney three signs (adult cases accounted for 85?)