多囊肾是一种常见的遗传性肾脏疾病 ,其两种类型均与儿科领域有着密切关系。临床早期常缺乏典型症状 ,B超的进展有助于早期诊断 ,确诊依靠基因连锁分析。传统的控制血压、调整饮食等手段的疗效不确定。争取早期诊治可以改善疾病的预后 Polycystic kidney disease is a common hereditary kidney disease, both types are closely related with the pediatric field. Often lack of typical early clinical symptoms, B-ultrasound contribute to the early diagnosis, diagnosis depends on genetic linkage analysis. Traditional control of blood pressure, adjust the diet and other means of uncertainty. Striving for early diagnosis and treatment can improve the prognosis of the disease