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患儿男,13岁。体检发现心脏杂音3个月,于1994年11月17日入院。体检:发育正常,无紫绀。胸骨左缘第二肋间可闻及3级收缩期杂音,震颤阳性,肺动脉第二心音明显减弱。肝脾未及。血压12/8kPa。心电图示电轴左偏,右室肥大。X线胸片示肺血减少,心外形增大,肺动脉段突出,右室肥大。心脏B超示右心室内径2cm,主肺动脉增宽达2.9cm,肺动脉瓣开放受限,跨瓣压差3.5kPa。诊断为先天性心脏病,肺动脉瓣狭窄。在全麻下手术,切开心包,心包腔内无粘连。见主肺动脉扩张,肺动脉根部可扪及震颤。肺动脉瓣处有一深凹切
Children male, 13 years old. Physical examination found heart murmur for 3 months, on November 17, 1994 admission. Physical examination: normal development, no cyanosis. The second intercostal sternal left margin can be heard and 3 systolic murmur, tremor positive pulmonary heart sound second significantly weakened. Liver and spleen not yet. Blood pressure 12 / 8kPa. ECG left axis deviation, right ventricular hypertrophy. X-ray showed decreased lung blood, heart shape increased pulmonary artery prominent, right ventricular hypertrophy. Heart B ultrasound showed right ventricular diameter 2cm, the main pulmonary artery widened up to 2.9cm, pulmonary valve open restricted, transvalvular pressure 3.5kPa. Diagnosis of congenital heart disease, pulmonary valve stenosis. Surgery under general anesthesia, incision pericardium, pericardial cavity without adhesions. See the main pulmonary artery dilatation, pulmonary artery palpable tremor. There is a deep concave at the pulmonary valve